Pulmonary Hypertension Associated with Stenosis or Atresia of Pulmonary Veins

Acute Pulmonary Vasodilator Testing and Long-Term Clinical Course in Segmental Pulmonary Vascular Disease

Liezl Domingo, H. Sonali Magdo, Ronald W. Day University of Utah and Primary Children’s Hospital.United States Pediatric CardiologyPediatr Cardiol 2018; 39: 501-508DOI: 10.1007/s00246-017-1780-9 AbstractResults of acute pulmonary vasodilator testing (AVT) and the outcome of medical therapy have not been described in patients with segmental pulmonary vascular disease (SPVD). We sought to compare the pulmonary vasodilatory effects […]

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Predictors of Serious Adverse Events and High-Level Cardiorespiratory Support in Patients Undergoing Transcatheter Pulmonary Vein Interventions

Jessica A. Barreto, Kimberlee Gauvreau, Diego Porras, Jesse J. Esch, Nicola Maschietto, Brian Quinn, Lisa Bergersen, Mary Stein, Ryan Callahan Harvard Medical School and Boston Children’s Hospital. University of Pennsylvania Perelman School of Medicine and Children’s Hospital of Philadelphia.United States Pediatric CardiologyPediatr Cardiol 2023;DOI: 10.1007/s00246-023-03129-6 AbstractPatients with pulmonary vein stenosis (PVS) often require frequent transcatheter pulmonary

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Surgical and Cardiac Catheterization Outcomes of Scimitar Syndrome Patients: A Three Decade Single-Center Experience

Emma Seymour, George Mallory, Raysa Morales-Demori Baylor College of Medicine and Texas Children’s Hospital.United States Pediatric CardiologyPediatr Cardiol 2023; 44: 579-586DOI: 10.1007/s00246-022-02965-2 AbstractScimitar syndrome (SS) is a rare congenital condition which includes partial anomalous pulmonary venous return (PAPVR) and a variable degree of pulmonary hypoplasia. We describe the clinical features, therapeutic approach and outcomes of patients

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Treatment and prognosis of Scimitar syndrome: A retrospective analysis in a single center of East China

Kai Wang, Xinyi Xu, Tingliang Liu, Wei Gao, Ying Guo Shanghai Children’s Medical Center and Shanghai Jiao Tong University. The First Affiliated Hospital of Wenzhou Medical University.China Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2022;DOI: 10.3389/fcvm.2022.973796 AbstractBackground: Scimitar syndrome is a rare congenital cardiovascular malformation; its optimal management remains controversial. This study aims to present the clinical experience

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Total Anomalous Pulmonary Venous Connection Repair: Single-Center Outcomes in a Lower-Middle Income Region

Praveen Reddy Bayya, Shruti Varghese, Jessin Puliparambil Jayashankar, Abish Sudhakar, Rakhi Balachandran, Brijesh Parayaru Kottayil, Balaji Srimurugan, Praveen Kerala Varma, Praveen Kumar Neema, R. Krishna Kumar Amrita Institute of Medical Sciences and Research CentreIndia World Journal for Pediatric and Congenital Heart SurgeryWorld J Pediatr Congenit Heart Surg 2022; 13: 458-465DOI: 10.1177/21501351221103492 AbstractBackground: The management of total anomalous

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Computed tomographic parenchymal lung findings in premature infants with pulmonary vein stenosis

Barry O’Callaghan, Jenny E. Zablah, Jason P. Weinman, Erin K. Englund, Gareth J. Morgan, D. Dunbar Ivy, Benjamin S. Frank, David Andrew Mong, LaDonna J. Malone, Lorna P. Browne Children’s Hospital Colorado, Aurora and University of Colorado Medical SchoolUnited States Pediatric RadiologyPediatr Radiol 2023;DOI: 10.1007/s00247-023-05673-y AbstractBackground: Developmental pulmonary vein pulmonary vein stenosis in the setting of prematurity

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Clinical Syndromic Phenotypes and the Potential Role of Genetics in Pulmonary Vein Stenosis

Abbas H. Zaidi, Jessica M. Yamada, David T. Miller, Kerry McEnaney, Christina Ireland, Amy E. Roberts, Kimberlee Gauvreau, Kathy J. Jenkins, Ming Hui Chen Boston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2021; 8DOI: 10.3390/children8020128 AbstractPulmonary vein stenosis (PVS) is a rare, frequently lethal disease with heterogeneous phenotypes and an unclear etiology. Limited studies have

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Primary pulmonary vein stenosis among premature infants with single-vessel disease

Eli Zettler, Brian K. Rivera, Corey Stiver, Brian Boe, Clifford Cua, Molly K. Ball, Charles V. Smith, Jonathan L. Slaughter, Bernadette Chen, Ryan Callahan, Carl H. Backes Nationwide Children’s Hospital and Ohio State University. University of Washington School of Medicine. Boston Children’s Hospital and Harvard Medical School.United States Journal of PerinatologyJ Perinatol 2021; 41: 1621-1626DOI: 10.1038/s41372-020-00830-9

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Infantile Scimitar Syndrome With Contralateral Pulmonary Vein Stenosis and Refractory Pulmonary Hypertension

Janelle Buysse, Ramya Deepthi Billa, Daniel McLennan, Ravi Ashwath, Aditya Badheka, Madhuradhar Chegondi University of Iowa Stead Family Children’s Hospital.United States CureusCureus 2021; 13DOI: 10.7759/cureus.17203 AbstractInfantile scimitar syndrome is associated with pulmonary hypertension which can be difficult to manage. We present a three-month-old infant with scimitar syndrome, who eventually developed refractory pulmonary hypertension, posing a significant

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Is This My Home? A Palliative Care Journey Through Life and Death in the NICU: A Case Report

Aurora Walters, Jordan Grosse Children’s Hospital ColoradoUnited States Advances in Neonatal CareAdv Neonatal Care 2020; 20: 127-135DOI: 10.1097/ANC.0000000000000697 AbstractBackground: With advancements in neonatology, patients in the neonatal intensive care unit (NICU) are living in the hospital with complex life-limiting illnesses until their first birthday or beyond. As palliative care (PC) becomes a standard of care in neonatology,

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