Pulmonary Hypertension Associated with Stenosis or Atresia of Pulmonary Veins

Multifactorial pulmonary hypertension in infantile scimitar syndrome

Damien Bonnet, Isabelle Szezepanski, Christophe Delacourt, Sophie Malkezadeh-Milani, Maryline Lévy Hôpital Necker-Enfants Malades, AP-HP, Université de ParisFrance Archives of Cardiovascular DiseaseArch Cardiovasc Dis 2022; 115: 142-150DOI: 10.1016/j.acvd.2022.01.004 AbstractBackground: Pulmonary hypertension in infantile scimitar syndrome is highly prevalent at diagnosis, and has a multifactorial origin.Aims: To analyse the constellation of anatomical anomalies and initial physiology, and their contribution […]

Multifactorial pulmonary hypertension in infantile scimitar syndrome Read More »

Management of Complex Pulmonary Vein Stenosis at Altitude Combining Comprehensive Percutaneous Interventional Treatment with Sirolimus, Pulmonary Hypertension Medications and Intraluminal Imaging with Optical Coherence Tomography

Michael J. Shorofsky, Gareth J. Morgan, Ernesto Mejia, Salvador A. Rodriguez, Megan Greene, Paige Sheaks, Dunbar Ivy, Jenny E. Zablah University of Colorado and Children’s Hospital Colorado.United States Pediatric CardiologyPediatr Cardiol 2023; Online ahead of printDOI: 10.1007/s00246-023-03102-3 AbstractBackground: Pulmonary vein stenosis (PVS) is a growing problem for the pediatric congenital heart population. Sirolimus has previously been shown

Management of Complex Pulmonary Vein Stenosis at Altitude Combining Comprehensive Percutaneous Interventional Treatment with Sirolimus, Pulmonary Hypertension Medications and Intraluminal Imaging with Optical Coherence Tomography Read More »

Pulmonary Vein Atresia: Feasibility of Initial Recanalization Attempts with Subsequent Follow-up

Varun Aggarwal, Gary E. Stapleton, Lindsay F. Eilers, Srinath Gowda, Manish Bansal, Athar M. Qureshi, Melissa K. Webb, Asra Khan, Henri Justino Baylor College of Medicine and Texas Children’s HospitalUnited States Current Problems in CardiologyCurr Probl Cardiol 2023; 48DOI: 10.1016/j.cpcardiol.2022.101463 AbstractPulmonary vein atresia (PVA) may lead to pulmonary hypertension, cardiac failure, and death. Transcatheter or surgical treatments have rarely been offered to this population because of perceived poor outcomes. We describe single center

Pulmonary Vein Atresia: Feasibility of Initial Recanalization Attempts with Subsequent Follow-up Read More »

Association between pulmonary vein stenosis and necrotizing enterocolitis or gastrointestinal pathology: A case-control study

Jennifer Duchon, Christiana Farkouh‑Karoleski, Dominique D. Bailey, Usha S. Krishnan Bronx Care Hospital System. Columbia University Irving Medical Center. Valley Health System.United States Annals of Pediatric CardiologyAnn Pediatr Cardiol 2022; 15: 13-19DOI: 10.4103/apc.apc_210_21 AbstractObjective: Pulmonary vein stenosis (PVS) is an emerging cause of pulmonary hypertension in preterm infants. It is an often lethal condition with poor long.term

Association between pulmonary vein stenosis and necrotizing enterocolitis or gastrointestinal pathology: A case-control study Read More »

Acute Pulmonary Vasodilator Testing and Long-Term Clinical Course in Segmental Pulmonary Vascular Disease

Liezl Domingo, H. Sonali Magdo, Ronald W. Day University of Utah and Primary Children’s Hospital.United States Pediatric CardiologyPediatr Cardiol 2018; 39: 501-508DOI: 10.1007/s00246-017-1780-9 AbstractResults of acute pulmonary vasodilator testing (AVT) and the outcome of medical therapy have not been described in patients with segmental pulmonary vascular disease (SPVD). We sought to compare the pulmonary vasodilatory effects

Acute Pulmonary Vasodilator Testing and Long-Term Clinical Course in Segmental Pulmonary Vascular Disease Read More »

Predictors of Serious Adverse Events and High-Level Cardiorespiratory Support in Patients Undergoing Transcatheter Pulmonary Vein Interventions

Jessica A. Barreto, Kimberlee Gauvreau, Diego Porras, Jesse J. Esch, Nicola Maschietto, Brian Quinn, Lisa Bergersen, Mary Stein, Ryan Callahan Harvard Medical School and Boston Children’s Hospital. University of Pennsylvania Perelman School of Medicine and Children’s Hospital of Philadelphia.United States Pediatric CardiologyPediatr Cardiol 2023;DOI: 10.1007/s00246-023-03129-6 AbstractPatients with pulmonary vein stenosis (PVS) often require frequent transcatheter pulmonary

Predictors of Serious Adverse Events and High-Level Cardiorespiratory Support in Patients Undergoing Transcatheter Pulmonary Vein Interventions Read More »

Surgical and Cardiac Catheterization Outcomes of Scimitar Syndrome Patients: A Three Decade Single-Center Experience

Emma Seymour, George Mallory, Raysa Morales-Demori Baylor College of Medicine and Texas Children’s Hospital.United States Pediatric CardiologyPediatr Cardiol 2023; 44: 579-586DOI: 10.1007/s00246-022-02965-2 AbstractScimitar syndrome (SS) is a rare congenital condition which includes partial anomalous pulmonary venous return (PAPVR) and a variable degree of pulmonary hypoplasia. We describe the clinical features, therapeutic approach and outcomes of patients

Surgical and Cardiac Catheterization Outcomes of Scimitar Syndrome Patients: A Three Decade Single-Center Experience Read More »

Treatment and prognosis of Scimitar syndrome: A retrospective analysis in a single center of East China

Kai Wang, Xinyi Xu, Tingliang Liu, Wei Gao, Ying Guo Shanghai Children’s Medical Center and Shanghai Jiao Tong University. The First Affiliated Hospital of Wenzhou Medical University.China Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2022;DOI: 10.3389/fcvm.2022.973796 AbstractBackground: Scimitar syndrome is a rare congenital cardiovascular malformation; its optimal management remains controversial. This study aims to present the clinical experience

Treatment and prognosis of Scimitar syndrome: A retrospective analysis in a single center of East China Read More »

Total Anomalous Pulmonary Venous Connection Repair: Single-Center Outcomes in a Lower-Middle Income Region

Praveen Reddy Bayya, Shruti Varghese, Jessin Puliparambil Jayashankar, Abish Sudhakar, Rakhi Balachandran, Brijesh Parayaru Kottayil, Balaji Srimurugan, Praveen Kerala Varma, Praveen Kumar Neema, R. Krishna Kumar Amrita Institute of Medical Sciences and Research CentreIndia World Journal for Pediatric and Congenital Heart SurgeryWorld J Pediatr Congenit Heart Surg 2022; 13: 458-465DOI: 10.1177/21501351221103492 AbstractBackground: The management of total anomalous

Total Anomalous Pulmonary Venous Connection Repair: Single-Center Outcomes in a Lower-Middle Income Region Read More »

Computed tomographic parenchymal lung findings in premature infants with pulmonary vein stenosis

Barry O’Callaghan, Jenny E. Zablah, Jason P. Weinman, Erin K. Englund, Gareth J. Morgan, D. Dunbar Ivy, Benjamin S. Frank, David Andrew Mong, LaDonna J. Malone, Lorna P. Browne Children’s Hospital Colorado, Aurora and University of Colorado Medical SchoolUnited States Pediatric RadiologyPediatr Radiol 2023;DOI: 10.1007/s00247-023-05673-y AbstractBackground: Developmental pulmonary vein pulmonary vein stenosis in the setting of prematurity

Computed tomographic parenchymal lung findings in premature infants with pulmonary vein stenosis Read More »