Pulmonary Hypertension Associated with Stenosis or Atresia of Pulmonary Veins

Clinical Syndromic Phenotypes and the Potential Role of Genetics in Pulmonary Vein Stenosis

Abbas H. Zaidi, Jessica M. Yamada, David T. Miller, Kerry McEnaney, Christina Ireland, Amy E. Roberts, Kimberlee Gauvreau, Kathy J. Jenkins, Ming Hui Chen Boston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2021; 8DOI: 10.3390/children8020128 AbstractPulmonary vein stenosis (PVS) is a rare, frequently lethal disease with heterogeneous phenotypes and an unclear etiology. Limited studies have […]

Clinical Syndromic Phenotypes and the Potential Role of Genetics in Pulmonary Vein Stenosis Read More »

Primary pulmonary vein stenosis among premature infants with single-vessel disease

Eli Zettler, Brian K. Rivera, Corey Stiver, Brian Boe, Clifford Cua, Molly K. Ball, Charles V. Smith, Jonathan L. Slaughter, Bernadette Chen, Ryan Callahan, Carl H. Backes Nationwide Children’s Hospital and Ohio State University. University of Washington School of Medicine. Boston Children’s Hospital and Harvard Medical School.United States Journal of PerinatologyJ Perinatol 2021; 41: 1621-1626DOI: 10.1038/s41372-020-00830-9

Primary pulmonary vein stenosis among premature infants with single-vessel disease Read More »

Infantile Scimitar Syndrome With Contralateral Pulmonary Vein Stenosis and Refractory Pulmonary Hypertension

Janelle Buysse, Ramya Deepthi Billa, Daniel McLennan, Ravi Ashwath, Aditya Badheka, Madhuradhar Chegondi University of Iowa Stead Family Children’s Hospital.United States CureusCureus 2021; 13DOI: 10.7759/cureus.17203 AbstractInfantile scimitar syndrome is associated with pulmonary hypertension which can be difficult to manage. We present a three-month-old infant with scimitar syndrome, who eventually developed refractory pulmonary hypertension, posing a significant

Infantile Scimitar Syndrome With Contralateral Pulmonary Vein Stenosis and Refractory Pulmonary Hypertension Read More »

Is This My Home? A Palliative Care Journey Through Life and Death in the NICU: A Case Report

Aurora Walters, Jordan Grosse Children’s Hospital ColoradoUnited States Advances in Neonatal CareAdv Neonatal Care 2020; 20: 127-135DOI: 10.1097/ANC.0000000000000697 AbstractBackground: With advancements in neonatology, patients in the neonatal intensive care unit (NICU) are living in the hospital with complex life-limiting illnesses until their first birthday or beyond. As palliative care (PC) becomes a standard of care in neonatology,

Is This My Home? A Palliative Care Journey Through Life and Death in the NICU: A Case Report Read More »

Pulmonary Vein Stenosis: Outcomes in Children With Congenital Heart Disease and Prematurity

Michael P. DiLorenzo, Ashley Santo, Jonathan J. Rome, Huayan Zhang, Jennifer A. Faerber, Laura Mercer-Rosa, Rachel K. Hopper The Children’s Hospital of Philadelphia. NewYork-Presbyterian/Morgan Stanley Children’s Hospital and Columbia University Irving Medical Center. Stanford University School of Medicine.United States Seminars in Thoracic and Cardiovascular SurgerySemin Thorac Cardiovasc Surg 2019; 31: 266-273DOI: 10.1053/j.semtcvs.2018.09.027 AbstractPulmonary vein stenosis (PVS)

Pulmonary Vein Stenosis: Outcomes in Children With Congenital Heart Disease and Prematurity Read More »

Intervening with the Nitric Oxide Pathway to Alleviate Pulmonary Hypertension in Pulmonary Vein Stenosis

Richard W. B. van Duin, Kelly Stam, André Uitterdijk, Beatrijs Bartelds, A. H. Jan Danser, Irwin K. M. Reiss, Dirk J. Duncker, Daphne Merkus Erasmus MC Rotterdam. Sophia Children’s Hospital. University Hospital, LMU Munich.Netherlands and Germany Journal of Clinical MedicineJ Clin Med 2019; 8DOI: 10.3390/jcm8081204 AbstractPulmonary hypertension (PH) as a result of pulmonary vein stenosis (PVS)

Intervening with the Nitric Oxide Pathway to Alleviate Pulmonary Hypertension in Pulmonary Vein Stenosis Read More »

Mortality in infants with bronchopulmonary dysplasia: Data from cardiac catheterization

Martina A. Steurer, Hythem Nawaytou, Elyssa Guslits, Elizabeth Colglazier, David Teitel, Jeffrey R. Fineman, Roberta L. Keller University of California, San Francisco.United States Pediatric PulmonologyPediatr Pulmonol 2019; 54: 804-813DOI: 10.1002/ppul.24297 AbstractRationale: Pulmonary hypertension (PH) is relatively common in infants with severe bronchopulmonary dysplasia (BPD), however, hemodynamic data and factors associated with mortality in this patient group are

Mortality in infants with bronchopulmonary dysplasia: Data from cardiac catheterization Read More »

Death or resolution: the “natural history” of pulmonary hypertension in bronchopulmonary dysplasia

Gabriel Altit, Shazia Bhombal, Rachel K. Hopper, Theresa A. Tacy, Jeffrey Feinstein McGill University and Montreal Children’s Hospital – McGill University Health Centre. Stanford University School of Medicine and Lucile Packard Children’s Hospital.Canada and United States Journal of PerinatologyJ Perinatol 2019; 39: 415-425DOI: 10.1038/s41372-018-0303-8 AbstractObjectives: The primary objective was to describe the early “natural history” of pulmonary

Death or resolution: the “natural history” of pulmonary hypertension in bronchopulmonary dysplasia Read More »

Outcomes and prognostic factors for postsurgical pulmonary vein stenosis in the current era

David Kalfa, Emre Belli, Emile Bacha, Virginie Lambert, Ducciodi Carlo, Martin Kostolny, Matej Nosal, Jurgen Horer, Jukka Salminen, Jean Rubay, Illya Yemets, Mark Hazekamp, Bohdan Maruszewski, George Sarris, Hakan Berggren, Tjark Ebels, Onur Baser, Francois Lacour-Gayet and the European Congenital Heart Surgeons Association Morgan Stanley Children’s Hospital of New York-Presbyterian and Columbia University. Marie Lannelongue

Outcomes and prognostic factors for postsurgical pulmonary vein stenosis in the current era Read More »

Progressive pulmonary vein stenosis in Down syndrome infant: a rare cause of pulmonary hypertension

Norazah Zahari, Joyce Darshinee Dom Sirisani University of Malaya.Malaysia Medical Journal of MalaysiaMed J Malaysia 2018; 73: 119-120DOI: Not available AbstractPulmonary veins stenosis in a Down Syndrome infant with normal connection pulmonary vein is rare and precise incidence of this disease is unknown. We report a case of progressive multiple pulmonary vein stenosis in a

Progressive pulmonary vein stenosis in Down syndrome infant: a rare cause of pulmonary hypertension Read More »