Article Type: Retrospective Observational Cohort Studies (>10 patients)

Right Ventricular Function Improves With Pulmonary Vasodilator Treatment in Pediatric Patients With Pulmonary Hypertension and Multivessel Pulmonary Vein Stenosis in a Single Center Cohort

Catherine M. Avitabile, Kimberly Butler, Antara Mondal, David B. Frank, Yan Wang, Devon Ash, Laura Mercer‐Rosa, Michael L. O’Byrne, Ryan Callahan University of Pennsylvania, Perelman School of Medicine and Children’s Hospital of Philadelphia.United States Pulmonary CirculationPulm Circ 2026; 16:DOI: 10.1002/pul2.70346 AbstractPulmonary hypertension (PH) and right ventricular (RV) dysfunction increase mortality in multivessel pediatric pulmonary vein stenosis […]

Right Ventricular Function Improves With Pulmonary Vasodilator Treatment in Pediatric Patients With Pulmonary Hypertension and Multivessel Pulmonary Vein Stenosis in a Single Center Cohort Read More »

Pulmonary Venous Decompressing Collaterals: Angiographic Characteristics and Impact on Outcomes in Pediatric Pulmonary Vein Stenosis

Ashish Saini, Hui Huang, Andrew Jergel, Rosemary Gray, Dennis W. Kim, James Kuo Children’s Healthcare of Atlanta and Emory University School of Medicine.United States Pediatric CardiologyPediatr Cardiol 2026;DOI: 10.1007/s00246-026-04350-9 AbstractPediatric pulmonary vein stenosis (PVS) is a rare, progressive condition associated with significant morbidity and mortality. While pulmonary venous decompressing collaterals (PVDC) have been described, their clinical

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Pulmonary vein stenosis after pediatric heart transplantation: incidence and risk factors

Hyun Soo Lee, Han Ki Park, Sang On Lee, Yu Rim Shin Severance Cardiovascular Hospital and Yonsei University College of Medicine.Republic of Korea Frontiers in SurgeryFront Surg 2026; 13: DOI: 10.3389/fsurg.2026.1820935 AbstractObjectives: Postoperative pulmonary vein stenosis (PVS) is an uncommon but potentially serious complication following pediatric heart transplantation. This study aimed to determine the prevalence of PVS

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Characteristics and outcomes of preterm infants with pulmonary vein stenosis in the contemporary era: a PHIS database analysis

Mohamed F. Elsisy, Fred Z. Lam, Mark M. Naguib, Mary E. Dees, James C. Gay, George T. Nicholson Monroe Carell Jr. Children’s Hospital at Vanderbilt. United States Journal of PerinatologyJ Perinatol 2026; DOI: 10.1038/s41372-026-02703-z AbstractBackground: Pulmonary vein stenosis (PVS) is increasingly recognized in preterm infants, yet data regarding characteristics and outcomes remain limited.Methods: A review of hospitalizations from

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Surgical and Catheter-Based Intervention in Pediatric Pulmonary Vein Stenosis

Daiji Takajo, Paul J. Critser, Awais Ashfaq, Russel Hirsch Cincinnati Children’s Hospital Medical Center and University of Cincinnati. University of Texas Southwestern Medical Center. United States Pediatric CardiologyPediatr Cardiol 2026; DOI: 10.1007/s00246-026-04266-4 AbstractBackground: Pulmonary vein stenosis (PVS) is a rare but serious condition in children, often requiring surgical or catheter-based interventions. The initial optimal treatment strategy remains

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Mutations in VCP cause Adams-Oliver syndrome with or without pulmonary hypertension

Anna Lehman, Sana Ahmed, Arezoo Mohajeri, Alison M. Berezuk, Dhiraj Mannar, Spencer Cholak, Katharine S. Tuttle, James T. Bennett, Jeanine Aparecida Magno, Mark Hannibal, Gordana Kovacevik, Vladimir Kuburovic, M.E. Suzanne Lewis, Oana Moldovan, Zoe Nelson, Salmo Raskin, Anthony M. Vandersteen, Jared C. Roach, Sriram Subramaniam, Millan S. Patel University of British Columbia. University of Washington

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Outcomes and Patency Following Surgical Repair of Previously Stented Pulmonary Veins in Pediatric Patients

Allison Beckham Davila, Mariana Chavez, Kimberlee Gauvreau, Christina Ireland, Kathy J. Jenkins, Michael Farias, Eric N. Feins, Christopher W. Baird Boston Children’s Hospital and Harvard Medical School. Lurie Children’s Hospital of Chicago and Feinberg School of Medicine.United States Annals of Thoracic SurgeryAnn Thorac Surg 2026;DOI: 10.1016/j.athoracsur.2026.03.056 AbstractBackground: The study objective was to evaluate surgical outcomes of patients

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Catheter and echocardiographic-focused management of primary pulmonary vein stenosis in premature infants: a single center 5-year experience

Keira Nassetta Conor P. O’Halloran, Emily Hoyt, Matthew Cornicelli, Nicolas Porta, Jeremy Fox, Alan W. Nugent, Paul Tannous, Amanda Hauck Ann and Robert H. Lurie Children’s Hospital of Chicago.United States Journal of PerinatologyJ Perinatol 2026; DOI: 10.1038/s41372-026-02611-2 AbstractBackground/objectives: We describe the outcomes of pulmonary vein stenosis treatment in a cohort of premature infants using an assertive percutaneous

Catheter and echocardiographic-focused management of primary pulmonary vein stenosis in premature infants: a single center 5-year experience Read More »

Quantification of 3-Dimensional Confluence-Atrial Morphology in Supracardiac Total Anomalous Pulmonary Venous Connection

Guocheng Shi, Meiping Huang, Yuchen Pei, Peng Huang, Chen Wen, Jin Shentu, Hao Zhang, Zhongqun Zhu, Yumin Zhong, Lisheng Wang, Huiwen Chen Shanghai Children’s Medical Center and Shanghai Jiao Tong University School of Medicine. Guangdong General Hospital. Hunan Children’s Hospital.China Journal of the American College of Cardiology AsiaJACC Asia 2024; 4: 594-606DOI: 10.1016/j.jacasi.2024.05.002 AbstractBackground: Pulmonary vein stenosis

Quantification of 3-Dimensional Confluence-Atrial Morphology in Supracardiac Total Anomalous Pulmonary Venous Connection Read More »

Impact of the pulmonary venous entry site morphology on postoperative pulmonary vein stenosis in total anomalous pulmonary venous connection patients

Szu-Yen Hu, Jing-Ren Ye, Heng-Wen Chou, Yih-Sharng Chen, Chung-I Chang, Ing-Sh Chiu, Chih-Ting Lin, Hsiao-En Tsai, Shyh-Jye Chen, Shu-Chien Huang National Taiwan University Hospital and National Taiwan University.Taiwan Journal of Formosan Medical AssociationJ Formos Med Assoc 2025; 124: 809-815DOI: 10.1016/j.jfma.2024.09.006 AbstractBackground: To evaluate the association between the pulmonary vein (PV) entry site morphology after total anomalous pulmonary

Impact of the pulmonary venous entry site morphology on postoperative pulmonary vein stenosis in total anomalous pulmonary venous connection patients Read More »