Article Type: Retrospective Observational Cohort Studies (>10 patients)

Surgical results of total anomalous pulmonary venous connection repair in 256 patients

Takeaki Harada, Toshihide Nakano, Shinichiro Oda, Hideaki Kado Fukuoka Children’s Hospital.Japan Interactive CardioVascular and Thoracic SurgeryInteract Cardiovasc Thorac Surg 2019; 8: 421-426DOI: 10.1093/icvts/ivy267 AbstractObjectives: This study was performed to analyse the surgical results of total anomalous pulmonary venous connection (TAPVC) repair at a single institution and to identify trends and variables associated with mortality and morbidity, particularly […]

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Total anomalous pulmonary venous connection: results of surgical repair of 100 patients at a single institution

Angela M. Kelle, Carl L. Backer, Jeffrey G. Gossett, Sunjay Kaushal, Constantine Mavroudis Northwestern University Feinberg School of Medicine and Children’s Memorial Hospital.United States Journal of Thoracic and Cardiovascular SurgeryJ Thorac Cardiovasc Surg 2010; 139: 1387-1394DOI: 10.1016/j.jtcvs.2010.02.024 AbstractObjective: Surgical repair of total anomalous pulmonary venous connection is associated with significant mortality and morbidity, especially in patients with

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The impact of right ventricular pressure and function on survival in patients with pulmonary vein stenosis

Michelle C. Sykes, Christina Ireland, Julia E. McSweeney, Emily Rosenholm, Kristofer G. Andren, Thomas J. Kulik Boston Children’s Hospital.United States Pulmonary CirculationPulm Circ 2018;DOI: 10.1177/2045894018776894 AbstractPulmonary vein stenosis (PVS) is associated with pulmonary hypertension (PH), but there is little information regarding the impact of PH on right ventricular (RV) systolic function and survival. We conducted a

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How is pulmonary arterial blood flow affected by pulmonary venous obstruction in children? A phase-contrast magnetic resonance study

Kevin S. Roman, Christian Kellenberger, Christopher K. Macgowan, John Coles, Andrew N. Redington, Lee N. Benson, Shi-Joon Yoo Hospital for Sick Children.Canada Pediatric RadiologyPediatr Radiol 2005; 35: 580-586DOI: 10.1007/s00247-004-1399-x AbstractBackground: Hemodynamic changes within a stenosed pulmonary vein might not reflect the severity of the obstruction if redistribution of pulmonary artery flow occurs.Objective: The purpose was to investigate flow

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Gadolinium-enhanced three-dimensional magnetic resonance angiography of pulmonary and systemic venous anomalies

Gerald F. Greil, Andrew J. Powell, Hans P. Gildein, Tal Geva Children’s Hospital, Boston.United States Journal of the American College of CardiologyJ Am Coll Cardiol 2002; 39: 335-341DOI: 10.1016/s0735-1097(01)01730-2 AbstractObjective: The goal of this study was to evaluate the diagnostic value of gadolinium (Gd)-enhanced three-dimensional (3D) magnetic resonance angiography (MRA) in patients with congenital and acquired anomalies

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Pulmonary vein stenosis and necrotising enterocolitis: is there a possible link with necrotising enterocolitis?

Howard J. Heching, Mariel Turner, Christiana Farkouh-Karoleski, Usha Krishnan Columbia University Medical Center.United States Archives of Diseases in Children Fetal and Neonatal EditionArch Dis Child Fetal Neonatal Ed 2014; 99: F282-F285DOI: 10.1136/archdischild-2013-304740 AbstractObjectives: While acquired pulmonary vein stenosis (PVS) is an often lethal anomaly with poor long-term prognosis and high mortality, little is known about the causes of this

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Bilateral disease and early age at presentation are associated with shorter survival in patients with congenital heart disease and intraluminal pulmonary vein stenosis

Sowmya Balasubramanian, Maliha Rehman, Kimberlee Gauvreau, Kathy J. Jenkins Children’s Hospital Boston.United States Congenital Heart DiseaseCongenit Heart Dis 2012; 7: 378-386DOI: 10.1111/j.1747-0803.2012.00647.x AbstractPurpose: Pulmonary vein stenosis (PVS) is a progressive disease that is frequently lethal. We have previously identified neoproliferation of myofibroblasts as the mechanism for progressive intraluminal PVS. PVS occurs in association with other congenital heart

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Systemic Sirolimus Therapy for Infants and Children With Pulmonary Vein Stenosis

Jay D. Patel, Michael Briones, Mansi Mandhani, Shannon Jones, Divya Suthar, Rosemary Gray, Joelle Pettus, Courtney McCraken, Amanda Thomas, Christopher J. Petit Emory University and Children’s Healthcare of AtlantaUnited States Journal of the American College of CardiologyJ Am Coll Cardiol 2021; 77: 2807-2818DOI: 10.1016/j.jacc.2021.04.013 AbstractBackground: Anatomic interventions for pulmonary vein stenosis (PVS) in infants and children have

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Multifactorial pulmonary hypertension in infantile scimitar syndrome

Damien Bonnet, Isabelle Szezepanski, Christophe Delacourt, Sophie Malkezadeh-Milani, Maryline Lévy Hôpital Necker-Enfants Malades, AP-HP, Université de ParisFrance Archives of Cardiovascular DiseaseArch Cardiovasc Dis 2022; 115: 142-150DOI: 10.1016/j.acvd.2022.01.004 AbstractBackground: Pulmonary hypertension in infantile scimitar syndrome is highly prevalent at diagnosis, and has a multifactorial origin.Aims: To analyse the constellation of anatomical anomalies and initial physiology, and their contribution

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Reintervention and mortality risk after total anomalous pulmonary venous connection repair

Kevin M. Beers, Christian P. Jacobson, Stewart R. Miller, David G. Lehenbauer, Elaine Maldonado, S. Adil Husain, John H. Calhoon University of Texas Health San Antonio.United States Cardiology in the YoungCardiol Young 2023; Online ahead of printDOI: 10.1017/S1047951122004280 AbstractBackground: Management of total anomalous pulmonary venous connections has been extensively studied to further improve outcomes. Our institution previously

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