Article Type: Retrospective Observational Cohort Studies (>10 patients)

How is pulmonary arterial blood flow affected by pulmonary venous obstruction in children? A phase-contrast magnetic resonance study

Kevin S. Roman, Christian Kellenberger, Christopher K. Macgowan, John Coles, Andrew N. Redington, Lee N. Benson, Shi-Joon Yoo Hospital for Sick Children.Canada Pediatric RadiologyPediatr Radiol 2005; 35: 580-586DOI: 10.1007/s00247-004-1399-x AbstractBackground: Hemodynamic changes within a stenosed pulmonary vein might not reflect the severity of the obstruction if redistribution of pulmonary artery flow occurs.Objective: The purpose was to investigate flow […]

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Gadolinium-enhanced three-dimensional magnetic resonance angiography of pulmonary and systemic venous anomalies

Gerald F. Greil, Andrew J. Powell, Hans P. Gildein, Tal Geva Children’s Hospital, Boston.United States Journal of the American College of CardiologyJ Am Coll Cardiol 2002; 39: 335-341DOI: 10.1016/s0735-1097(01)01730-2 AbstractObjective: The goal of this study was to evaluate the diagnostic value of gadolinium (Gd)-enhanced three-dimensional (3D) magnetic resonance angiography (MRA) in patients with congenital and acquired anomalies

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Pulmonary vein stenosis and necrotising enterocolitis: is there a possible link with necrotising enterocolitis?

Howard J. Heching, Mariel Turner, Christiana Farkouh-Karoleski, Usha Krishnan Columbia University Medical Center.United States Archives of Diseases in Children Fetal and Neonatal EditionArch Dis Child Fetal Neonatal Ed 2014; 99: F282-F285DOI: 10.1136/archdischild-2013-304740 AbstractObjectives: While acquired pulmonary vein stenosis (PVS) is an often lethal anomaly with poor long-term prognosis and high mortality, little is known about the causes of this

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Bilateral disease and early age at presentation are associated with shorter survival in patients with congenital heart disease and intraluminal pulmonary vein stenosis

Sowmya Balasubramanian, Maliha Rehman, Kimberlee Gauvreau, Kathy J. Jenkins Children’s Hospital Boston.United States Congenital Heart DiseaseCongenit Heart Dis 2012; 7: 378-386DOI: 10.1111/j.1747-0803.2012.00647.x AbstractPurpose: Pulmonary vein stenosis (PVS) is a progressive disease that is frequently lethal. We have previously identified neoproliferation of myofibroblasts as the mechanism for progressive intraluminal PVS. PVS occurs in association with other congenital heart

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Systemic Sirolimus Therapy for Infants and Children With Pulmonary Vein Stenosis

Jay D. Patel, Michael Briones, Mansi Mandhani, Shannon Jones, Divya Suthar, Rosemary Gray, Joelle Pettus, Courtney McCraken, Amanda Thomas, Christopher J. Petit Emory University and Children’s Healthcare of AtlantaUnited States Journal of the American College of CardiologyJ Am Coll Cardiol 2021; 77: 2807-2818DOI: 10.1016/j.jacc.2021.04.013 AbstractBackground: Anatomic interventions for pulmonary vein stenosis (PVS) in infants and children have

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Multifactorial pulmonary hypertension in infantile scimitar syndrome

Damien Bonnet, Isabelle Szezepanski, Christophe Delacourt, Sophie Malkezadeh-Milani, Maryline Lévy Hôpital Necker-Enfants Malades, AP-HP, Université de ParisFrance Archives of Cardiovascular DiseaseArch Cardiovasc Dis 2022; 115: 142-150DOI: 10.1016/j.acvd.2022.01.004 AbstractBackground: Pulmonary hypertension in infantile scimitar syndrome is highly prevalent at diagnosis, and has a multifactorial origin.Aims: To analyse the constellation of anatomical anomalies and initial physiology, and their contribution

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Reintervention and mortality risk after total anomalous pulmonary venous connection repair

Kevin M. Beers, Christian P. Jacobson, Stewart R. Miller, David G. Lehenbauer, Elaine Maldonado, S. Adil Husain, John H. Calhoon University of Texas Health San Antonio.United States Cardiology in the YoungCardiol Young 2023; Online ahead of printDOI: 10.1017/S1047951122004280 AbstractBackground: Management of total anomalous pulmonary venous connections has been extensively studied to further improve outcomes. Our institution previously

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Pulmonary Vein Atresia: Feasibility of Initial Recanalization Attempts with Subsequent Follow-up

Varun Aggarwal, Gary E. Stapleton, Lindsay F. Eilers, Srinath Gowda, Manish Bansal, Athar M. Qureshi, Melissa K. Webb, Asra Khan, Henri Justino Baylor College of Medicine and Texas Children’s HospitalUnited States Current Problems in CardiologyCurr Probl Cardiol 2023; 48DOI: 10.1016/j.cpcardiol.2022.101463 AbstractPulmonary vein atresia (PVA) may lead to pulmonary hypertension, cardiac failure, and death. Transcatheter or surgical treatments have rarely been offered to this population because of perceived poor outcomes. We describe single center

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Acute Pulmonary Vasodilator Testing and Long-Term Clinical Course in Segmental Pulmonary Vascular Disease

Liezl Domingo, H. Sonali Magdo, Ronald W. Day University of Utah and Primary Children’s Hospital.United States Pediatric CardiologyPediatr Cardiol 2018; 39: 501-508DOI: 10.1007/s00246-017-1780-9 AbstractResults of acute pulmonary vasodilator testing (AVT) and the outcome of medical therapy have not been described in patients with segmental pulmonary vascular disease (SPVD). We sought to compare the pulmonary vasodilatory effects

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Benefit of stereoscopic volume rendering for the identification of pediatric pulmonary vein stenosis from CT angiography

Michelle Noga, Ross Cockburn, Jiali Luan, Deepa Krishnaswamy, Kumaradevan Punithakumar University of Alberta. Mazankowski Alberta Heart Institute. University of Manitoba. Dalhousie University.Canada PLOS Digital HealthPLOS Digit Health 2023; 2DOI: 10.1371/journal.pdig.0000215 AbstractThe use of three-dimensional (3D) technologies in medical practice is increasing; however, its use is largely untested. One 3D technology, stereoscopic volume-rendered 3D display, can improve

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