Article Type: Retrospective Observational Cohort Studies (>10 patients)

Bilateral disease and early age at presentation are associated with shorter survival in patients with congenital heart disease and intraluminal pulmonary vein stenosis

Sowmya Balasubramanian, Maliha Rehman, Kimberlee Gauvreau, Kathy J. Jenkins Children’s Hospital Boston.United States Congenital Heart DiseaseCongenit Heart Dis 2012; 7: 378-386DOI: 10.1111/j.1747-0803.2012.00647.x AbstractPurpose: Pulmonary vein stenosis (PVS) is a progressive disease that is frequently lethal. We have previously identified neoproliferation of myofibroblasts as the mechanism for progressive intraluminal PVS. PVS occurs in association with other congenital heart […]

Bilateral disease and early age at presentation are associated with shorter survival in patients with congenital heart disease and intraluminal pulmonary vein stenosis Read More »

Systemic Sirolimus Therapy for Infants and Children With Pulmonary Vein Stenosis

Jay D. Patel, Michael Briones, Mansi Mandhani, Shannon Jones, Divya Suthar, Rosemary Gray, Joelle Pettus, Courtney McCraken, Amanda Thomas, Christopher J. Petit Emory University and Children’s Healthcare of AtlantaUnited States Journal of the American College of CardiologyJ Am Coll Cardiol 2021; 77: 2807-2818DOI: 10.1016/j.jacc.2021.04.013 AbstractBackground: Anatomic interventions for pulmonary vein stenosis (PVS) in infants and children have

Systemic Sirolimus Therapy for Infants and Children With Pulmonary Vein Stenosis Read More »

Multifactorial pulmonary hypertension in infantile scimitar syndrome

Damien Bonnet, Isabelle Szezepanski, Christophe Delacourt, Sophie Malkezadeh-Milani, Maryline Lévy Hôpital Necker-Enfants Malades, AP-HP, Université de ParisFrance Archives of Cardiovascular DiseaseArch Cardiovasc Dis 2022; 115: 142-150DOI: 10.1016/j.acvd.2022.01.004 AbstractBackground: Pulmonary hypertension in infantile scimitar syndrome is highly prevalent at diagnosis, and has a multifactorial origin.Aims: To analyse the constellation of anatomical anomalies and initial physiology, and their contribution

Multifactorial pulmonary hypertension in infantile scimitar syndrome Read More »

Reintervention and mortality risk after total anomalous pulmonary venous connection repair

Kevin M. Beers, Christian P. Jacobson, Stewart R. Miller, David G. Lehenbauer, Elaine Maldonado, S. Adil Husain, John H. Calhoon University of Texas Health San Antonio.United States Cardiology in the YoungCardiol Young 2023; Online ahead of printDOI: 10.1017/S1047951122004280 AbstractBackground: Management of total anomalous pulmonary venous connections has been extensively studied to further improve outcomes. Our institution previously

Reintervention and mortality risk after total anomalous pulmonary venous connection repair Read More »

Pulmonary Vein Atresia: Feasibility of Initial Recanalization Attempts with Subsequent Follow-up

Varun Aggarwal, Gary E. Stapleton, Lindsay F. Eilers, Srinath Gowda, Manish Bansal, Athar M. Qureshi, Melissa K. Webb, Asra Khan, Henri Justino Baylor College of Medicine and Texas Children’s HospitalUnited States Current Problems in CardiologyCurr Probl Cardiol 2023; 48DOI: 10.1016/j.cpcardiol.2022.101463 AbstractPulmonary vein atresia (PVA) may lead to pulmonary hypertension, cardiac failure, and death. Transcatheter or surgical treatments have rarely been offered to this population because of perceived poor outcomes. We describe single center

Pulmonary Vein Atresia: Feasibility of Initial Recanalization Attempts with Subsequent Follow-up Read More »

Acute Pulmonary Vasodilator Testing and Long-Term Clinical Course in Segmental Pulmonary Vascular Disease

Liezl Domingo, H. Sonali Magdo, Ronald W. Day University of Utah and Primary Children’s Hospital.United States Pediatric CardiologyPediatr Cardiol 2018; 39: 501-508DOI: 10.1007/s00246-017-1780-9 AbstractResults of acute pulmonary vasodilator testing (AVT) and the outcome of medical therapy have not been described in patients with segmental pulmonary vascular disease (SPVD). We sought to compare the pulmonary vasodilatory effects

Acute Pulmonary Vasodilator Testing and Long-Term Clinical Course in Segmental Pulmonary Vascular Disease Read More »

Benefit of stereoscopic volume rendering for the identification of pediatric pulmonary vein stenosis from CT angiography

Michelle Noga, Ross Cockburn, Jiali Luan, Deepa Krishnaswamy, Kumaradevan Punithakumar University of Alberta. Mazankowski Alberta Heart Institute. University of Manitoba. Dalhousie University.Canada PLOS Digital HealthPLOS Digit Health 2023; 2DOI: 10.1371/journal.pdig.0000215 AbstractThe use of three-dimensional (3D) technologies in medical practice is increasing; however, its use is largely untested. One 3D technology, stereoscopic volume-rendered 3D display, can improve

Benefit of stereoscopic volume rendering for the identification of pediatric pulmonary vein stenosis from CT angiography Read More »

Predictors of Serious Adverse Events and High-Level Cardiorespiratory Support in Patients Undergoing Transcatheter Pulmonary Vein Interventions

Jessica A. Barreto, Kimberlee Gauvreau, Diego Porras, Jesse J. Esch, Nicola Maschietto, Brian Quinn, Lisa Bergersen, Mary Stein, Ryan Callahan Harvard Medical School and Boston Children’s Hospital. University of Pennsylvania Perelman School of Medicine and Children’s Hospital of Philadelphia.United States Pediatric CardiologyPediatr Cardiol 2023;DOI: 10.1007/s00246-023-03129-6 AbstractPatients with pulmonary vein stenosis (PVS) often require frequent transcatheter pulmonary

Predictors of Serious Adverse Events and High-Level Cardiorespiratory Support in Patients Undergoing Transcatheter Pulmonary Vein Interventions Read More »

Long-term results of the Warden procedure for right partial anomalous pulmonary venous connection

Clément Dubost, Carine Pavy, Pierre Maminirina, Nadir Benbrik, Olivier Baron Hospital for Children and Adolescents.France Cardiology in the YoungCardiol Young 2023; 33: 457-462DOI: 10.1017/S1047951122001184 AbstractIntroduction: Surgery is considered as the first-line therapeutic strategy of partial anomalous pulmonary venous connection. The Warden technique has very good short-term results. The aim of this study is to evaluate the stability

Long-term results of the Warden procedure for right partial anomalous pulmonary venous connection Read More »

Surgical and Cardiac Catheterization Outcomes of Scimitar Syndrome Patients: A Three Decade Single-Center Experience

Emma Seymour, George Mallory, Raysa Morales-Demori Baylor College of Medicine and Texas Children’s Hospital.United States Pediatric CardiologyPediatr Cardiol 2023; 44: 579-586DOI: 10.1007/s00246-022-02965-2 AbstractScimitar syndrome (SS) is a rare congenital condition which includes partial anomalous pulmonary venous return (PAPVR) and a variable degree of pulmonary hypoplasia. We describe the clinical features, therapeutic approach and outcomes of patients

Surgical and Cardiac Catheterization Outcomes of Scimitar Syndrome Patients: A Three Decade Single-Center Experience Read More »