Right Heart Failure Associated with Stenosis or Atresia of Pulmonary Veins

Extracorporeal Life Support (ECLS) for Pulmonary Vein Stenosis Interventions

Stephanie M. Tsoi, Roberta L. Keller, Loren D. Sacks, Vinod Sebastian, Sanjeev A. Datar, Michael A. Smith, Jason Boehme, Jeffrey R. Fineman, Elena K. Amin University of California San Francisco.United States Pediatric CardiologyPediatr Cardiol 2026;DOI: 10.1007/s00246-026-04434-6 AbstractPediatric pulmonary vein stenosis (PVS) is associated with high morbidity and mortality. We describe a case series of pediatric patients […]

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Right Ventricular Function Improves With Pulmonary Vasodilator Treatment in Pediatric Patients With Pulmonary Hypertension and Multivessel Pulmonary Vein Stenosis in a Single Center Cohort

Catherine M. Avitabile, Kimberly Butler, Antara Mondal, David B. Frank, Yan Wang, Devon Ash, Laura Mercer‐Rosa, Michael L. O’Byrne, Ryan Callahan University of Pennsylvania, Perelman School of Medicine and Children’s Hospital of Philadelphia.United States Pulmonary CirculationPulm Circ 2026; 16:DOI: 10.1002/pul2.70346 AbstractPulmonary hypertension (PH) and right ventricular (RV) dysfunction increase mortality in multivessel pediatric pulmonary vein stenosis

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Case Report: Post-Total anomalous pulmonary venous connection pulmonary hypertension – novel treatment using sirolimus and atrial flow regulator implantation

Stasa Krasic, Antony Hermuzi, Ivan Dizdarevic, Vesna Topic, Nevena Djorovic, Mihail Basa, Vladislav Vukomanovic Mother and Child Health Institute of Serbia and University of Belgrade. Freeman Hospital and Newcastle upon Tyne Hospitals NHS Foundation Trust.Serbia and United Kingdom Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2026; 13:DOI: 10.3389/fcvm.2026.1783773 AbstractObjective: In patients who have undergone surgical repair of TAPVC

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Swine model of chronic postcapillary pulmonary hypertension with right ventricular remodeling: long-term characterization by cardiac catheterization, magnetic resonance, and pathology

Daniel Pereda, Ana Garcia-Alvarez, Damián Sánchez-Quintana, Mario Nuño, Leticia Fernández-Friera, Rodrigo Fernández-Jiménez, José Manuel García Ruíz, Elena Sandoval, Jaume Aguero, Manuel Castellá. Roger J. Hajjar, Valentín Fuster, Borja Ibáñez Centro Nacional de Investigaciones Cardiovasculares Carlos III.Spain Journal of Cardiovascular Translational ResearchJ Cardiovasc Transl Res 2014; 7: 494-506DOI: 10.1007/s12265-014-9564-6 AbstractPulmonary hypertension (PH) is prevalent and carries high

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Pulmonary Hypertension With Unilateral Pulmonary Vein Atresia

Bong-Joon Kim, Soo-Jin Kim, Sung-Il Im, Hyunsu Kim, Jung-Ho Heo, Tae-Won Jang Kosin University Gospel Hospital, Kosin University College of Medicine.Republic of Korea International Journal of Heart FailureInt J Heart Fail 2023; 5: 102-105DOI: 10.36628/ijhf.2023.0003 AbstractAbstract Not Available CategoryAbsence or Atresia of Normal Pulmonary Venous ConnectionsPulmonary Hypertension Associated with Stenosis or Atresia of Pulmonary VeinsRight Heart

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Mortality Patterns in Pediatric Pulmonary Vein Stenosis: Insights Into Right Ventricular Systolic Pressure Associations

Daiji Takajo, Paul J. Critser, Michelle Cash, Melissa Magness, Russel Hirsch Cincinnati Children’s Hospital Medical Center and University of Cincinnati.United States Journal of the American Heart AssociationJ Am Heart Assoc 2025;DOI: 10.1161/JAHA.124.037908 AbstractBackground: Pulmonary vein stenosis in children is associated with a poor prognosis. However, the cause and risk factors for mortality remain uncertain.Methods: This retrospective, single-center study

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Lung transplantation for congenital pulmonary vein stenosis

Eric N. Mendeloff, Thomas L. Spray, Charles B. Huddleston, Nancy D. Bridges, Charles B. Canter, George B. Mallory, Jr. Washington University School of Medicine.United States Annals of Thoracic SurgeryAnn Thorac Surg 1995; 60: 903-906DOI: 10.1016/0003-4975(95)00543-t AbstractBackground: Congenital pulmonary vein stenosis is a uniformly fatal disease when left untreated. Transcatheter techniques (for example, balloon dilation and stent placement)

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De Novo and Progressive Pulmonary Vein Stenosis Following Pediatric Heart Transplantation: A Multicenter Retrospective Study

Arene Butto, Conor O’Halloran, James Kuo, Anna Joong, Amanda L. Hauck, Alan Nugent, William Mahle, Paul Tannous Children’s Healthcare of Atlanta. Lurie Children’s Hospital.United States Pediatric TransplantationPediatr Transplant 2024; 28:DOI: 10.1111/petr.14828 AbstractBackground: Pulmonary vein stenosis (PVS) is a rare condition in which neointimal proliferation leads to venous and arterial hypertension. Little is known about PVS after heart

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Rare cause of cardiac failure in an infant

Claudio Henriques, Helena Andrade, Antonio Pires Paediatric Hospital.Portugal Cardiology in the YoungCardiol Young 2019; 29: 711-713DOI: 10.1017/S1047951119000428 AbstractCongenital stenosis of the pulmonary veins is a rare condition whose outcome is guarded despite the available treatment options. We report a case of a 6-month-old infant with significant stenosis of all four pulmonary veins. CategoryStenosis or Obstruction of

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The impact of right ventricular pressure and function on survival in patients with pulmonary vein stenosis

Michelle C. Sykes, Christina Ireland, Julia E. McSweeney, Emily Rosenholm, Kristofer G. Andren, Thomas J. Kulik Boston Children’s Hospital.United States Pulmonary CirculationPulm Circ 2018;DOI: 10.1177/2045894018776894 AbstractPulmonary vein stenosis (PVS) is associated with pulmonary hypertension (PH), but there is little information regarding the impact of PH on right ventricular (RV) systolic function and survival. We conducted a

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