Stenosis or Obstruction of Normal Pulmonary Venous Connections

Therapeutic Targets for Pediatric Pulmonary Vein Stenosis: Insights from Animal Models

Siqi She, Debao Li, Qi Sun, Lincai Ye Shanghai Children’s Medical Center and Shanghai Jiao Tong University School of Medicine. Children’s Hospital of Fudan University and National Children’s Medical Center.China ChildrenChildren 2026; 13:DOI: 10.3390/children13050677 AbstractPulmonary vein stenosis (PVS) is a rare and devastating condition affecting infants and children, characterized by progressive intimal hyperplasia, myofibroblast proliferation, and […]

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Pathogenesis, Evaluation, and Management of Pulmonary Vein Stenosis: JACC Review Topic of the Week

Trevor Simard, Dhruv Sarma, William R. Miranda, Charles Jain, Jason H. Anderson, Jeremy D. Collins, Abdallah El Sabbagh, Aravdeep Jhand, Tobias Peikert, Guy S. Reeder, Thomas M. Munger, Douglas L. Packer, David R. Holmes Mayo Clinic.United States Journal of the American College of CardiologyJ Am Coll Cardiol 2023; 81: 2361-2373DOI: 10.1016/j.jacc.2023.04.016 AbstractPulmonary vein stenosis (PVS) can

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Pulmonary arterial hypertension caused by compression of the left lower pulmonary vein in children

Li Chen, Cheng Wang, Jiachen Li, Lizhi Lv, Yongtao Wu, Gang Li, Guofeng Xing, Xiaoyong Jing, Zhimin Liu, Qiang Wang Beijing Anzhen Hospital and Capital Medical University.  Fuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College.China Journal of Cardiothoracic SurgeryJ Cardiothorac Surg 2026;DOI: 10.1186/s13019-026-04085-x AbstractObjectives To investigate, through

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Characteristics and outcomes of preterm infants with pulmonary vein stenosis in the contemporary era: a PHIS database analysis

Mohamed F. Elsisy, Fred Z. Lam, Mark M. Naguib, Mary E. Dees, James C. Gay, George T. Nicholson Monroe Carell Jr. Children’s Hospital at Vanderbilt. United States Journal of PerinatologyJ Perinatol 2026; DOI: 10.1038/s41372-026-02703-z AbstractBackground: Pulmonary vein stenosis (PVS) is increasingly recognized in preterm infants, yet data regarding characteristics and outcomes remain limited.Methods: A review of hospitalizations from

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Surgical and Catheter-Based Intervention in Pediatric Pulmonary Vein Stenosis

Daiji Takajo, Paul J. Critser, Awais Ashfaq, Russel Hirsch Cincinnati Children’s Hospital Medical Center and University of Cincinnati. University of Texas Southwestern Medical Center. United States Pediatric CardiologyPediatr Cardiol 2026; DOI: 10.1007/s00246-026-04266-4 AbstractBackground: Pulmonary vein stenosis (PVS) is a rare but serious condition in children, often requiring surgical or catheter-based interventions. The initial optimal treatment strategy remains

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Pediatric Pulmonary Vein Stenosis and Treatment

Joice Prodigios, Stephanie El Omeiri, Marcus Meneses, Bethelhem Belachew, Hansel J. Otero, David M. Biko, Jordan B. Rapp Children’s Hospital of Philadelphia and Perelman School of Medicine at The University of Pennsylvania.United States Seminars in RoentenologySemin Roentenol 2025; DOI: 10.1053/j.ro.2025.09.006 AbstractPulmonary vein stenosis (PVS) is an uncommon but often progressive condition in children, associated with high

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Adams-Oliver syndrome with widespread CMTC and fatal pulmonary vascular disease

Ophelia Entsir Dadzie, Lidia Tyszczuk, Susan E. Holder, Fernanda Teixeira, Aikaterina Charakida, Julia Scarisbrick, Anthony Chu Hammersmith Hospital.United Kingdom Pediatric DermatologyPediatr Dermatol 2007; 24: 651-653DOI: 10.1111/j.1525-1470.2007.00556.x AbstractWe report a neonate with cutis marmorata telangiectatica congenita and clinical features of Adams-Oliver syndrome in association with severe pulmonary vascular disease. We provide an overview of cutis marmorata telangiectatica

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Abnormal Pericyte Recruitment as a Cause for Pulmonary Hypertension in Adams–Oliver Syndrome

Millan S. Patel, Glenn P. Taylor, Simi Bharya, Nouriya Al-Sanna’a, Ian Adatia, David Chitayat, M.E. Suzanne Lewis, Derek G. Human Hospital for Sick Children and University of Toronto. Children’s and Women’s Health Center of British Columbia and University of British Columbia. Canada American Journal of Medical Genetics Am J Med Genet 2004; 129A: 294-299DOI: 10.1002/ajmg.a.30221 AbstractAdams-Oliver

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Mutations in VCP cause Adams-Oliver syndrome with or without pulmonary hypertension

Anna Lehman, Sana Ahmed, Arezoo Mohajeri, Alison M. Berezuk, Dhiraj Mannar, Spencer Cholak, Katharine S. Tuttle, James T. Bennett, Jeanine Aparecida Magno, Mark Hannibal, Gordana Kovacevik, Vladimir Kuburovic, M.E. Suzanne Lewis, Oana Moldovan, Zoe Nelson, Salmo Raskin, Anthony M. Vandersteen, Jared C. Roach, Sriram Subramaniam, Millan S. Patel University of British Columbia. University of Washington

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Outcomes and Patency Following Surgical Repair of Previously Stented Pulmonary Veins in Pediatric Patients

Allison Beckham Davila, Mariana Chavez, Kimberlee Gauvreau, Christina Ireland, Kathy J. Jenkins, Michael Farias, Eric N. Feins, Christopher W. Baird Boston Children’s Hospital and Harvard Medical School. Lurie Children’s Hospital of Chicago and Feinberg School of Medicine.United States Annals of Thoracic SurgeryAnn Thorac Surg 2026;DOI: 10.1016/j.athoracsur.2026.03.056 AbstractBackground: The study objective was to evaluate surgical outcomes of patients

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