Stenosis or Obstruction of Normal Pulmonary Venous Connections

Preliminary findings on the use of intravascular ultrasound in the assessment of pediatric pulmonary vein stenosis

Ryan Callahan, Kathy J. Jenkins, Zachary Gauthier, Kimberlee Gauvreau, Diego Porras Boston Children’s Hospital and Harvard Medical SchoolUnited States Catheterization and Cardiovascular InterventionsCatheter Cardiovasc Interv 2021; 97: E362-E370DOI: 10.1002/ccd.29264 AbstractObjective: Determine the feasibility of performing intravascular ultrasound (IVUS) in pediatric pulmonary vein stenosis (PVS) and investigate whether IVUS can delineate the mechanism of PVS.Background: The use of IVUS […]

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Intravascular Ultrasound for Pulmonary Vein Stenosis Interventions in Congenital Heart Disease

Samantha A. Kops, Danielle Strah, Kwan S. Lee, Michael D. Seckeler University of Arizona.United States Journal of Invasive CardiologyJ Invasive Cardiol 2021; 33: E259-E262 AbstractObjective: Pulmonary vein stenosis (PVS) is aggressive, with high morbidity and mortality. Surgical and catheter interventions yield modest success, at best. Refinements in catheter interventions could potentially improve outcomes in this patient

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Infantile Scimitar Syndrome With Contralateral Pulmonary Vein Stenosis and Refractory Pulmonary Hypertension

Janelle Buysse, Ramya Deepthi Billa, Daniel McLennan, Ravi Ashwath, Aditya Badheka, Madhuradhar Chegondi University of Iowa Stead Family Children’s Hospital.United States CureusCureus 2021; 13DOI: 10.7759/cureus.17203 AbstractInfantile scimitar syndrome is associated with pulmonary hypertension which can be difficult to manage. We present a three-month-old infant with scimitar syndrome, who eventually developed refractory pulmonary hypertension, posing a significant

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This and that: management of Tetralogy of Fallot and pulmonary vein stenosis in an infant-a case report

Christopher P. Scott, Kamel Shibbani, Christopher A. Caldarone, Daniel McLennan Children’s Wisconsin. University of Iowa Stead Family Children’s Hospital. Texas Children’s Hospital.United States European Heart Journal Case ReportsEur Heart J Case Rep 2021; 5DOI: 10.1093/ehjcr/ytab429 AbstractBackground: Tetralogy of Fallot (TOF) is the most common congenital cyanotic cardiac lesion. Pulmonary vein stenosis occurs much less commonly and remains

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Effectiveness of posterior aortopexy for the left pulmonary vein obstruction between the left atrium and the descending aorta

Kwang Ho Choi, Hyungtae Kim, Si Chan Sung, Hyoung Doo Lee, Hoon Ko, Joung-Hee Byun Pusan National University Yangsan Hospital.Republic of Korea Journal of Cardiac SurgeryJ Card Surg 2021; 36: 2644-2650DOI: 10.1111/jocs.15596 AbstractBackground: Left pulmonary vein (PV) obstruction can occur due to compression between the left atrium (LA) and the descending aorta (DA). One of the effective

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Longer Exposure to Left-to-Right Shunts Is a Risk Factor for Pulmonary Vein Stenosis in Patients with Trisomy 21

Connie Choi, Kimberlee Gauvreau, Philip Levy, Ryan Callahan, Kathy J. Jenkins, Minghui Chen Harvard Medical School and Boston Children’s Hospital.United States ChildrenChildren 2021; 8DOI: 10.3390/children8010019 AbstractWe conducted a study to determine whether patients born with Trisomy 21 and left-to-right shunts who develop pulmonary vein stenosis (PVS) have a longer exposure to shunt physiology compared to those

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Treatment of Congenital and Acquired Pulmonary Vein Stenosis

Patcharapong Suntharos, Lourdes R. Prieto Nicklaus Children’s Hospital.United States Current Cardiology ReportsCurr Cardiol Rep 2020; 22DOI: 10.1007/s11886-020-01395-x AbstractPurpose of review: Pulmonary vein stenosis (PVS) is a rare entity that until the last 2 decades was seen primarily in infants and children. Percutaneous and surgical interventions have limited success due to relentless restenosis, and mortality remains high. In

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Progress in Pulmonary Vein Stenosis: Lessons from Success in Treating Pulmonary Arterial Hypertension

Kathy J. Jenkins, Jeffrey R. Fineman Boston Children’s Hospital. University of California, San Francisco.United States ChildrenChildren 2022; 9DOI: 10.3390/children9060799 AbstractPulmonary vein stenosis (PVS) is a rare and poorly understood condition that can be classified as primary, acquired, status-post surgical repair of PVS, and/or associated with developmental lung disease. Immunohistochemical studies demonstrate that obstruction of the large

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Systemic Sirolimus to Prevent In-Stent Stenosis in Pediatric Pulmonary Vein Stenosis

Ryan Callahan, Jesse J. Esch, Grace Wang, Christina M. Ireland, Kimberlee Gauvreau, Kathy J. Jenkins Boston Children’s Hospital and Harvard Medical School.United States Pediatric CardiologyPediatr Cardiol 2020; 41: 282-289DOI: 10.1007/s00246-019-02253-6 AbstractEvaluate the efficacy of systemic sirolimus (rapamycin) in preventing in-stent stenosis (ISS) in pediatric intraluminal pulmonary vein stenosis (PVS). Report the adverse events related to sirolimus

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Diagnostic performance of CT angiography to detect pulmonary vein stenosis in children

Christian A. Barrera, David Saul, Jordan B. Rapp, Christopher L. Smith, Ammie M. White, David M. Biko, Hansel J. Otero The Children’s Hospital of Philadelphia and University of Pennsylvania.United States International Journal of Cardiovascular ImagingInt J Cardiovasc Imaging 2020; 36: 141-147DOI: 10.1007/s10554-019-01693-8 AbstractTo assess the diagnostic efficiency of CT angiography (CTA) to detect pulmonary vein stenosis

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