Stenosis or Obstruction of Normal Pulmonary Venous Connections

Pulmonary Vein Stenosis: Incremental Knowledge Gains to Improve Outcomes

Rachel D. Vanderlaan, Christopher A. Caldarone Hospital for Sick Children. Texas Children’s Hospital.Canada and United States ChildrenChildren 2021; 8DOI: 10.3390/children8060481 AbstractPulmonary vein stenosis remains a considerable clinical challenge, with high mortality still present in children with progressive disease. In this review, we discuss the clinical spectrum of pulmonary vein stenosis and what is known about the […]

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Primary Pulmonary Vein Stenosis: A New Look at a Rare but Challenging Disease

Aditya V. Jadcherla, Carl H. Backes, Clifford L. Cua, Charles V. Smith, Philip T. Levy, Molly K. Ball Nationwide Children’s Hospital and Ohio State University College of Medicine. University of Washington School of Medicine. Harvard Medical School and Boston Children’s Hospital.United States NeoReviewsNeoreviews 2021; 22: e296-e308DOI: 10.1542/neo.22-5-e296 AbstractPrimary pulmonary vein stenosis (PPVS) represents a rare but

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Pulmonary Vein Stenosis: A Rare Disease with a Global Reach

Jennifer Schramm, Sivakumar Sivalingam, Guillermo E. Moreno, Dinh Quang Le Thanh, Kimberlee Gauvreau, Kaitlin Doherty-Schmeck, Kathy J. JenkinsChildren’s National Hospital. National Heart Institute. Hospital de Pediatría “Professor Dr. Juan P. Garrahan”. Children’s Hospital 1. Boston Children’s Hospital, Boston.United States, Malaysia, Argentina, Vietnam ChildrenChildren 2021; 8DOI: 10.3390/children8030198 AbstractPulmonary vein stenosis (PVS) is a rare, but high mortality

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Correlation of Intravascular Ultrasound with Histology in Pediatric Pulmonary Vein Stenosis

Ryan Callahan, Zachary Gauthier, Shuhei Toba, Stephen P. Sanders, Diego Porras, Sara O. Vargas Boston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2021; 8DOI: 10.3390/children8030193 AbstractPreliminary intravascular ultrasound (IVUS) images of suspected pediatric intraluminal pulmonary vein stenosis (PVS) demonstrate wall thickening. It is unclear how the IVUS-delineated constituents of wall thickening correlate with the histology.

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Lung and Pleural Findings of Children with Pulmonary Vein Stenosis with and without Aspiration: MDCT Evaluation

Abbey J. Winant, Ryan Callahan, Sara O. Vargas, Kathy J. Jenkins, Vanessa Rameh, Patrick R. Johnston, Maria Niccum, Mirjam L. Keochakian, Edward Y. Lee Boston Children’s Hospital and Harvard Medical School. Children’s Hospital of Philadelphia.United States ChildrenChildren 2022; 9DOI: 10.3390/children9040543 AbstractPurpose: To retrospectively compare the lung and pleural findings in children with pulmonary vein stenosis (PVS)

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Pleuropulmonary MDCT Findings: Comparison between Children with Pulmonary Vein Stenosis and Prematurity-Related Lung Disease

Abbey J. Winant, Sara O. Vargas, Kathy J. Jenkins, Ryan Callahan, Vanessa Rameh, Katie A. Krone, Patrick R. Johnston, Mirjam L. Keochakian, Edward Y. Lee Boston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2022; 9DOI: 10.3390/children9030355 AbstractPurpose: To retrospectively compare the pleuropulmonary MDCT findings in children with pulmonary vein stenosis (PVS) and prematurity-related lung disease

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Outcomes in Establishing Individual Vessel Patency for Pediatric Pulmonary Vein Stenosis

Ryan Callahan, Kimberlee Gauvreau, Audrey C. Marshall, Laureen M. Sena, Christopher W. Baird, Christina M. Ireland, Kerry McEnaney, Elsa C. Bjornlund, Juliana T. Mendonca, Kathy J. Jenkins Boston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2021; 8DOI: 10.3390/children8030210 AbstractThe purpose of this study was to determine what patient and pulmonary vein characteristics at the diagnosis

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Aspiration Is Associated with Poor Treatment Response in Pediatric Pulmonary Vein Stenosis

Maria Niccum, Ryan Callahan, Kimberlee Gauvreau, Kathy J. Jenkins Boston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2021; 8DOI: 10.3390/children8090783 AbstractIntraluminal pulmonary vein stenosis is a disease with significant morbidity and mortality, though recent progress has been made using multimodal therapy with antiproliferative agents. The aim of this study was to evaluate the association between

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Patient and Family-Centered Care for Pediatric Intraluminal Pulmonary Vein Stenosis: Case of a 3 Year Old Patient with Focus on Nurse Practitioner Role

Christina M. Ireland, Ryan Callahan, Kathy J. Jenkins Boston Children’s Hospital, Boston and Harvard Medical School.United States ChildrenChildren 2021; 8DOI: 10.3390/children8070567 AbstractA nurse practitioner’s experience in managing children with intraluminal pulmonary vein stenosis. A case study of a 3-year-old patient with multi-vessel intraluminal pulmonary vein stenosis. CategoryStenosis or Obstruction of Normal Pulmonary Venous ConnectionsMultidisciplinary Care Year

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Clinical Syndromic Phenotypes and the Potential Role of Genetics in Pulmonary Vein Stenosis

Abbas H. Zaidi, Jessica M. Yamada, David T. Miller, Kerry McEnaney, Christina Ireland, Amy E. Roberts, Kimberlee Gauvreau, Kathy J. Jenkins, Ming Hui Chen Boston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2021; 8DOI: 10.3390/children8020128 AbstractPulmonary vein stenosis (PVS) is a rare, frequently lethal disease with heterogeneous phenotypes and an unclear etiology. Limited studies have

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