Stenosis or Obstruction of Pulmonary Veins Following Surgical Repair of Anomalous Pulmonary Venous Connections

Bilateral disease and early age at presentation are associated with shorter survival in patients with congenital heart disease and intraluminal pulmonary vein stenosis

Sowmya Balasubramanian, Maliha Rehman, Kimberlee Gauvreau, Kathy J. Jenkins Children’s Hospital Boston.United States Congenital Heart DiseaseCongenit Heart Dis 2012; 7: 378-386DOI: 10.1111/j.1747-0803.2012.00647.x AbstractPurpose: Pulmonary vein stenosis (PVS) is a progressive disease that is frequently lethal. We have previously identified neoproliferation of myofibroblasts as the mechanism for progressive intraluminal PVS. PVS occurs in association with other congenital heart […]

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A prospective phase II trial of vinblastine and methotrexate in multivessel intraluminal pulmonary vein stenosis in infants and children

Maliha Rehman, Kathy J. Jenkins, Amy L. Juraszek, Jean A. Connor, Kimberlee Gauvreau, Muhammad Muneeb, Laureen M. Sena, Steven D. Colan, Terry Saia, Mark W. Kieran Children’s Hospital, Boston.United States Congenital Heart DiseaseCongenit Heart Dis 2011; 6: 608-623DOI: 10.1111/j.1747-0803.2011.00574.x AbstractObjective: To determine the safety and efficacy of the chemotherapeutic agents vinblastine and methotrexate in the treatment of

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Intraluminal Pulmonary Vein Stenosis in Children: A “New” Lesion

Viviane G. Nasr, Ryan Callahan, Zachary Wichner, Kirsten C. Odegard, James A. DiNardo Boston Children’s Hospital.United States Anesthesia and AnalgesiaAnesth Analges 2019; 129: 27-40DOI: 10.1213/ANE.0000000000003924 AbstractPulmonary vein stenosis (PVS) is a rare disorder that leads to progressive narrowing of the extrapulmonary veins. PVS has been reported in both children and adults and in its worse iteration

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Systemic Sirolimus Therapy for Infants and Children With Pulmonary Vein Stenosis

Jay D. Patel, Michael Briones, Mansi Mandhani, Shannon Jones, Divya Suthar, Rosemary Gray, Joelle Pettus, Courtney McCraken, Amanda Thomas, Christopher J. Petit Emory University and Children’s Healthcare of AtlantaUnited States Journal of the American College of CardiologyJ Am Coll Cardiol 2021; 77: 2807-2818DOI: 10.1016/j.jacc.2021.04.013 AbstractBackground: Anatomic interventions for pulmonary vein stenosis (PVS) in infants and children have

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Multifactorial pulmonary hypertension in infantile scimitar syndrome

Damien Bonnet, Isabelle Szezepanski, Christophe Delacourt, Sophie Malkezadeh-Milani, Maryline Lévy Hôpital Necker-Enfants Malades, AP-HP, Université de ParisFrance Archives of Cardiovascular DiseaseArch Cardiovasc Dis 2022; 115: 142-150DOI: 10.1016/j.acvd.2022.01.004 AbstractBackground: Pulmonary hypertension in infantile scimitar syndrome is highly prevalent at diagnosis, and has a multifactorial origin.Aims: To analyse the constellation of anatomical anomalies and initial physiology, and their contribution

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Management of Complex Pulmonary Vein Stenosis at Altitude Combining Comprehensive Percutaneous Interventional Treatment with Sirolimus, Pulmonary Hypertension Medications and Intraluminal Imaging with Optical Coherence Tomography

Michael J. Shorofsky, Gareth J. Morgan, Ernesto Mejia, Salvador A. Rodriguez, Megan Greene, Paige Sheaks, Dunbar Ivy, Jenny E. Zablah University of Colorado and Children’s Hospital Colorado.United States Pediatric CardiologyPediatr Cardiol 2023; Online ahead of printDOI: 10.1007/s00246-023-03102-3 AbstractBackground: Pulmonary vein stenosis (PVS) is a growing problem for the pediatric congenital heart population. Sirolimus has previously been shown

Management of Complex Pulmonary Vein Stenosis at Altitude Combining Comprehensive Percutaneous Interventional Treatment with Sirolimus, Pulmonary Hypertension Medications and Intraluminal Imaging with Optical Coherence Tomography Read More »

Reintervention and mortality risk after total anomalous pulmonary venous connection repair

Kevin M. Beers, Christian P. Jacobson, Stewart R. Miller, David G. Lehenbauer, Elaine Maldonado, S. Adil Husain, John H. Calhoon University of Texas Health San Antonio.United States Cardiology in the YoungCardiol Young 2023; Online ahead of printDOI: 10.1017/S1047951122004280 AbstractBackground: Management of total anomalous pulmonary venous connections has been extensively studied to further improve outcomes. Our institution previously

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Pulmonary Vein Atresia: Feasibility of Initial Recanalization Attempts with Subsequent Follow-up

Varun Aggarwal, Gary E. Stapleton, Lindsay F. Eilers, Srinath Gowda, Manish Bansal, Athar M. Qureshi, Melissa K. Webb, Asra Khan, Henri Justino Baylor College of Medicine and Texas Children’s HospitalUnited States Current Problems in CardiologyCurr Probl Cardiol 2023; 48DOI: 10.1016/j.cpcardiol.2022.101463 AbstractPulmonary vein atresia (PVA) may lead to pulmonary hypertension, cardiac failure, and death. Transcatheter or surgical treatments have rarely been offered to this population because of perceived poor outcomes. We describe single center

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Long-term results of the Warden procedure for right partial anomalous pulmonary venous connection

Clément Dubost, Carine Pavy, Pierre Maminirina, Nadir Benbrik, Olivier Baron Hospital for Children and Adolescents.France Cardiology in the YoungCardiol Young 2023; 33: 457-462DOI: 10.1017/S1047951122001184 AbstractIntroduction: Surgery is considered as the first-line therapeutic strategy of partial anomalous pulmonary venous connection. The Warden technique has very good short-term results. The aim of this study is to evaluate the stability

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Surgical and Cardiac Catheterization Outcomes of Scimitar Syndrome Patients: A Three Decade Single-Center Experience

Emma Seymour, George Mallory, Raysa Morales-Demori Baylor College of Medicine and Texas Children’s Hospital.United States Pediatric CardiologyPediatr Cardiol 2023; 44: 579-586DOI: 10.1007/s00246-022-02965-2 AbstractScimitar syndrome (SS) is a rare congenital condition which includes partial anomalous pulmonary venous return (PAPVR) and a variable degree of pulmonary hypoplasia. We describe the clinical features, therapeutic approach and outcomes of patients

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