Stenosis or Obstruction of Pulmonary Veins Following Surgical Repair of Anomalous Pulmonary Venous Connections

The many faces and outcomes of pulmonary vein stenosis in early childhood

Tilman Humpl, Jeffrey Fineman, Athar M. Qureshi University Children’s Hospital Berne. University of California, San Francisco. Texas Children’s Hospital and Baylor College of Medicine.Switzerland and United States Pediatric PulmonologyPediatr Pulmonol 2021; 56: 649-655DOI: 10.1002/ppul.24848 AbstractPulmonary vein stenosis is a rare and poorly understood condition causing obstruction of the large pulmonary veins and of blood flow from […]

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Pulmonary Vein Stenosis: Moving From Past Pessimism to Future Optimism

Daniel I. McLennan, Elyan C. Ruiz Solano, Stephanie S. Handler, Joy Lincoln, Michael E. Mitchell, Edward C. Kirkpatrick Medical College of Wisconsin.United States Frontiers in PediatricsFront Pediatr 2021;DOI: 10.3389/fped.2021.747812 AbstractPulmonary Vein Stenosis (PVS) is a rare disease with a prevalence of around 1. 7 cases per 100,000 children under 2 years old. Treatment options for this

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Pulmonary Vein Stenosis: Incremental Knowledge Gains to Improve Outcomes

Rachel D. Vanderlaan, Christopher A. Caldarone Hospital for Sick Children. Texas Children’s Hospital.Canada and United States ChildrenChildren 2021; 8DOI: 10.3390/children8060481 AbstractPulmonary vein stenosis remains a considerable clinical challenge, with high mortality still present in children with progressive disease. In this review, we discuss the clinical spectrum of pulmonary vein stenosis and what is known about the

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Pulmonary Vein Stenosis: A Rare Disease with a Global Reach

Jennifer Schramm, Sivakumar Sivalingam, Guillermo E. Moreno, Dinh Quang Le Thanh, Kimberlee Gauvreau, Kaitlin Doherty-Schmeck, Kathy J. JenkinsChildren’s National Hospital. National Heart Institute. Hospital de Pediatría “Professor Dr. Juan P. Garrahan”. Children’s Hospital 1. Boston Children’s Hospital, Boston.United States, Malaysia, Argentina, Vietnam ChildrenChildren 2021; 8DOI: 10.3390/children8030198 AbstractPulmonary vein stenosis (PVS) is a rare, but high mortality

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Correlation of Intravascular Ultrasound with Histology in Pediatric Pulmonary Vein Stenosis

Ryan Callahan, Zachary Gauthier, Shuhei Toba, Stephen P. Sanders, Diego Porras, Sara O. Vargas Boston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2021; 8DOI: 10.3390/children8030193 AbstractPreliminary intravascular ultrasound (IVUS) images of suspected pediatric intraluminal pulmonary vein stenosis (PVS) demonstrate wall thickening. It is unclear how the IVUS-delineated constituents of wall thickening correlate with the histology.

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Lung and Pleural Findings of Children with Pulmonary Vein Stenosis with and without Aspiration: MDCT Evaluation

Abbey J. Winant, Ryan Callahan, Sara O. Vargas, Kathy J. Jenkins, Vanessa Rameh, Patrick R. Johnston, Maria Niccum, Mirjam L. Keochakian, Edward Y. Lee Boston Children’s Hospital and Harvard Medical School. Children’s Hospital of Philadelphia.United States ChildrenChildren 2022; 9DOI: 10.3390/children9040543 AbstractPurpose: To retrospectively compare the lung and pleural findings in children with pulmonary vein stenosis (PVS)

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Outcomes in Establishing Individual Vessel Patency for Pediatric Pulmonary Vein Stenosis

Ryan Callahan, Kimberlee Gauvreau, Audrey C. Marshall, Laureen M. Sena, Christopher W. Baird, Christina M. Ireland, Kerry McEnaney, Elsa C. Bjornlund, Juliana T. Mendonca, Kathy J. Jenkins Boston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2021; 8DOI: 10.3390/children8030210 AbstractThe purpose of this study was to determine what patient and pulmonary vein characteristics at the diagnosis

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“Half-uncovered technique” to secure larger stents for postoperative pulmonary vein stenosis

Hiroaki Kise, Takanari Fujii, Hideshi Tomita Showa University.Japan Cardiology in the YoungCardiol Young 2022; 32: 1327-1329DOI: 10.1017/S1047951121004790 AbstractAlthough larger stent placement could be effective for pulmonary vein stenosis, stents extrusion tends to occur due to caliber narrowing, small landing area, and the slippery nature. We placed stents with diameter ≧8 mm for four stenotic lesions using

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Aspiration Is Associated with Poor Treatment Response in Pediatric Pulmonary Vein Stenosis

Maria Niccum, Ryan Callahan, Kimberlee Gauvreau, Kathy J. Jenkins Boston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2021; 8DOI: 10.3390/children8090783 AbstractIntraluminal pulmonary vein stenosis is a disease with significant morbidity and mortality, though recent progress has been made using multimodal therapy with antiproliferative agents. The aim of this study was to evaluate the association between

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Secondary Pulmonary Vein Stenosis Due to Total Anomalous Pulmonary Venous Connection Repair in Children: Extravascular MDCT Findings

Edward Y. Lee, Sara O. Vargas, Kathy J. Jenkins, Ryan Callahan, Halley J. Park, Zachary Gauthier, Abbey J. WinantBoston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2021; 8DOI: 10.3390/children8090726 AbstractPurpose: To evaluate extravascular findings on thoracic MDCT angiography in secondary pulmonary vein stenosis (PVS) due to total anomalous pulmonary venous connection (TAPVC) repair in children.Materials and

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