Age Focus: Pediatric

Adams-Oliver syndrome with widespread CMTC and fatal pulmonary vascular disease

Ophelia Entsir Dadzie, Lidia Tyszczuk, Susan E. Holder, Fernanda Teixeira, Aikaterina Charakida, Julia Scarisbrick, Anthony Chu Hammersmith Hospital.United Kingdom Pediatric DermatologyPediatr Dermatol 2007; 24: 651-653DOI: 10.1111/j.1525-1470.2007.00556.x AbstractWe report a neonate with cutis marmorata telangiectatica congenita and clinical features of Adams-Oliver syndrome in association with severe pulmonary vascular disease. We provide an overview of cutis marmorata telangiectatica […]

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Abnormal Pericyte Recruitment as a Cause for Pulmonary Hypertension in Adams–Oliver Syndrome

Millan S. Patel, Glenn P. Taylor, Simi Bharya, Nouriya Al-Sanna’a, Ian Adatia, David Chitayat, M.E. Suzanne Lewis, Derek G. Human Hospital for Sick Children and University of Toronto. Children’s and Women’s Health Center of British Columbia and University of British Columbia. Canada American Journal of Medical Genetics Am J Med Genet 2004; 129A: 294-299DOI: 10.1002/ajmg.a.30221 AbstractAdams-Oliver

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Outcomes and Patency Following Surgical Repair of Previously Stented Pulmonary Veins in Pediatric Patients

Allison Beckham Davila, Mariana Chavez, Kimberlee Gauvreau, Christina Ireland, Kathy J. Jenkins, Michael Farias, Eric N. Feins, Christopher W. Baird Boston Children’s Hospital and Harvard Medical School. Lurie Children’s Hospital of Chicago and Feinberg School of Medicine.United States Annals of Thoracic SurgeryAnn Thorac Surg 2026;DOI: 10.1016/j.athoracsur.2026.03.056 AbstractBackground: The study objective was to evaluate surgical outcomes of patients

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Catheter and echocardiographic-focused management of primary pulmonary vein stenosis in premature infants: a single center 5-year experience

Keira Nassetta Conor P. O’Halloran, Emily Hoyt, Matthew Cornicelli, Nicolas Porta, Jeremy Fox, Alan W. Nugent, Paul Tannous, Amanda Hauck Ann and Robert H. Lurie Children’s Hospital of Chicago.United States Journal of PerinatologyJ Perinatol 2026; DOI: 10.1038/s41372-026-02611-2 AbstractBackground/objectives: We describe the outcomes of pulmonary vein stenosis treatment in a cohort of premature infants using an assertive percutaneous

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Computational Predictive Modeling of Surgical Outcomes in Total Anomalous Pulmonary Venous Connection: Assessing the Impact of Pulmonary Venous Confluence Size on Preoperative Planning

Jie Jin, Zhuo Shi, Qiang Gao, Jing Yu, Irina Jin, Jiawei Liang, Xiangming Fan Children’s Hospital, Zhejiang University School of Medicine. Technical University of Moldova. China and Moldova Journal of Cardiovascular Translational ResearchJ Cardiovasc Transl Res 2025; 19: DOI: 10.1007/s12265-025-10725-9 AbstractTo develop a predictive model for optimal anastomosis sizing in TAPVC surgery, focusing on the role

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Long-term outcomes of individualised repair in patients with primary pulmonary vein stenosis

Zhangwei Wang, Yang Yang Beijing Children’s Hospital, National Children’s Medical Center and Capital Medical University.China Cardiology in the YoungCardiol Young 2025; DOI: 10.1017/S1047951124026180 AbstractObjectives: Primary pulmonary vein stenosis is a rare congenital heart condition and carries a poor prognosis. Various surgical techniques have been introduced to treat primary pulmonary vein stenosis. However, there is no consensus on

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Atrial thrombus after total anomalous pulmonary venous connection repair

Noriyoshi Ebuoka, Hidetsugu Asai, Sachiko Kimura, Tsuyoshi Tachibana Hokkaido Medical Center for Child Health and Rehabilitation. Kanagawa Children’s Medical Center.Japan Asian Cardiovascular and Thoracic AnnalsAsian Cardiovasc Thorac Ann 2024; 32: 314-316DOI: 10.1177/02184923241256408 AbstractA 6-year-old boy had previously undergone total anomalous pulmonary venous connection repair and postoperative pulmonary vein stenosis release. Magnetic resonance imaging revealed blood stasis

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New Era of Measurable Surgical Risk Predictor by 3D Quantitative CT on Pulmonary Venous Return

Shyh-Jye Chen National Taiwan University Hospital and Children’s Hospital.Taiwan Journal of the American College of Cardiology AsiaJACC Asia 2024; 4: 607-608DOI: 10.1016/j.jacasi.2024.06.001 AbstractAbstract Not Available CategoryStenosis or Obstruction of Pulmonary Veins Following Surgical Repair of Anomalous Pulmonary Venous ConnectionsDiagnostic Testing. Noninvasive Year of Publication: 2024 Age Focus: Pediatric Article Type: Editorial or Letter Article Access: Free

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Quantification of 3-Dimensional Confluence-Atrial Morphology in Supracardiac Total Anomalous Pulmonary Venous Connection

Guocheng Shi, Meiping Huang, Yuchen Pei, Peng Huang, Chen Wen, Jin Shentu, Hao Zhang, Zhongqun Zhu, Yumin Zhong, Lisheng Wang, Huiwen Chen Shanghai Children’s Medical Center and Shanghai Jiao Tong University School of Medicine. Guangdong General Hospital. Hunan Children’s Hospital.China Journal of the American College of Cardiology AsiaJACC Asia 2024; 4: 594-606DOI: 10.1016/j.jacasi.2024.05.002 AbstractBackground: Pulmonary vein stenosis

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Impact of the pulmonary venous entry site morphology on postoperative pulmonary vein stenosis in total anomalous pulmonary venous connection patients

Szu-Yen Hu, Jing-Ren Ye, Heng-Wen Chou, Yih-Sharng Chen, Chung-I Chang, Ing-Sh Chiu, Chih-Ting Lin, Hsiao-En Tsai, Shyh-Jye Chen, Shu-Chien Huang National Taiwan University Hospital and National Taiwan University.Taiwan Journal of Formosan Medical AssociationJ Formos Med Assoc 2025; 124: 809-815DOI: 10.1016/j.jfma.2024.09.006 AbstractBackground: To evaluate the association between the pulmonary vein (PV) entry site morphology after total anomalous pulmonary

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