Age Focus: Pediatric

A New Variant in the GATA6 Gene Associated with Tracheoesophageal Fistula, Pulmonary Vein Stenosis, and Neonatal Diabetes

Flaminia Pugnaloni, Ludovica Martini, Domenico Umberto De Rose, Francesca Landolfo, Paola Giliberti, Rosario Ruta, Antonio Novelli, Novella Rapini, Fabrizio Barbetti, Alessandra Toscano, Andrea Conforti, Pietro Bagolan, Irma Capolupo, Andrea Dotta “Bambino Gesù” Children’s Hospital Istituto di Ricovero e Cura a Carattere Scientifico. University of Rome “Tor Vergata”. Italy Hormone Research in PaediatricsHorm Res Paediatr 2025; […]

A New Variant in the GATA6 Gene Associated with Tracheoesophageal Fistula, Pulmonary Vein Stenosis, and Neonatal Diabetes Read More »

Combination Chemotherapy in Severe Pulmonary Vein Stenosis-A Case Series

Gabriel Krivenko, Karen Iacono, David Nykanen, Robyn Keen, Robert Sutphin, Michael Farias University of Central Florida. Orlando Health Arnold Palmer Hospital for Children. Boston Children’s Hospital.United States ChildrenChildren 2023; 10: DOI: 10.3390/children10020364 AbstractPulmonary vein stenosis results from a proliferative process that leads to the progressive obstruction of venous return to the left atrium. It is often

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Early Experience With Reverse Double Switch Operation for the Borderline Left Heart

Brandi Braud Scully, Eric N. Feins, Wayne Tworetzky, Sunil Ghelani, Rebecca Beroukhim, Pedro J. Del Nido, Sitaram M. Emani Boston Children’s Hospital and Harvard Medical School.United States Seminars in Thoracic and Cardiovascular SurgerySemin Thorac Cardiovasc Surg 2024; 36: 67-79DOI: 10.1053/j.semtcvs.2022.09.009 AbstractThis study reviews our early experience with the “reverse” double switch operation (R-DSO) for borderline left

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Tricuspid Valve Blood Cysts Mimicking Thrombus or Vegetation on Echocardiogram in a Neonate

Takato Yamasaki, Rebecca Beroukhim, Stephen Sanders, Chrystalle Katte Carreon Boston Children’s Hospital and Harvard Medical School. Mie University Graduate School of Medicine. United States and Japan Pediatric CardiologyPediatr Cardiol 2023; 44: 245-248DOI: 10.1007/s00246-022-02978-x AbstractA 2-month-old male infant, born premature with a birth weight of 865 g, was found to have a tricuspid valve mass mimicking thrombus

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Case report: Rescue treatment with add-on selexipag in a preterm infant with suprasystemic pulmonary hypertension, pulmonary capillary hemangiomatosis, and isolated pulmonary vein stenosis

Hosan Hasan, Klea Hysko, Thomas Jack, Jens Dingemann, Martin Wetzke, Georg Hansmann Hannover Medical School. European Pediatric Pulmonary Vascular Disease Network.Germany Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2022; 9: DOI: 10.3389/fcvm.2022.984698 AbstractAn extremely dystrophic, premature female infant, born at 25 3/7 weeks of gestational age (birth weight: 430 g) with severe pulmonary hypertension (PH), was admitted

Case report: Rescue treatment with add-on selexipag in a preterm infant with suprasystemic pulmonary hypertension, pulmonary capillary hemangiomatosis, and isolated pulmonary vein stenosis Read More »

Application of sutureless technique in total anomalous pulmonary venous connection repair

Zhangwei Wang, Nan Ding, Hanlu Yi, Yaobin Zhu, Zhiqiang Li, Daole Yan, Xiaofeng Li, Song Bai Beijing Children’s Hospital, Capital Medical University and National Children’s Medical Center.China Journal of Cardiac SurgeryJ Card Surg 2022; 37: 3769-3775DOI: 10.1111/jocs.16843 AbstractThe sutureless technique was initially used for the treatment of postoperative pulmonary vein obstruction (PVO) in patients with total

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Transconduit approach for pulmonary vein stenting in an extracardiac Fontan and plastic bronchitis case

Kumiyo Matsuo, Masaki Hirose, Hisaaki Aoki, Futoshi Kayatani Osaka Women’s and Children’s Hospital.Japan British Medical Journals Case ReportsBMJ Case Rep 2022; 13: DOI: 10.1136/bcr-2022-250565 AbstractPlastic bronchitis (PB) is a rare but severe complication in patients following the Fontan operation, the final palliative procedure for single ventricle heart disease. PB is characterised by the formation of rubbery

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Neonatal sutureless pericardial marsupialization for isolated iatrogenic pulmonary vein stenosis

Tomoyuki Iwase, Rajnish K. Garg, Mahmoud A. Al Soufi, Roberto M. Di Donato Al Jalila Children’s Hospital. United Arab Emirates Journal of Cardiac SurgeryJ Card Surg 2022; 37: 3932-3934DOI: 10.1111/jocs.16861 AbstractA 12-day-old girl underwent extended end-to-end aortic arch reconstruction with proximal pulmonary autograft patch augmentation on moderately hypothermic cardiopulmonary bypass. At the end of the procedure,

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Expanded Polytetrafluoroethylene Patching for Recurrent Pulmonary Venous Obstructions

Tomonari Shimoda, Bryan J. Mathis, Hideyuki Kato, Muneaki Matsubara, Yasuyuki Suzuki, Yuji Hiramatsu University of Tsukuba. Japan Annals of Thoracic SurgeryAnn Thorac Surg 2022; 114: e335-e337DOI: 10.1016/j.athoracsur.2022.01.014 AbstractRecurrent postoperative pulmonary venous obstruction after total anomalous pulmonary venous connection repair is a challenging complication. Here, we present such a case that required 4 reoperations, focusing on a

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Artificial Roofing for Recurrent Pulmonary Vein Stenosis

Andrew B. Gladstone, Emile A. Bacha Morgan Stanley Children’s Hospital of New York and Columbia University.United States Annals of Thoracic SurgeryAnn Thorac Surg 2022; 114: DOI: 10.1016/j.athoracsur.2022.02.074 AbstractAbstract Not Available CategorySurgical Interventions for Pulmonary Venous Obstruction After the Onset of Disease Year of Publication: 2022 Age Focus: Pediatric Article Type: Editorial or Letter Article Access: Free

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